Table 1 Demographic, clinical features and treatment of GSD patients
From: Clinical features and current management experience in Gorham-Stout disease: a systematic review
Variables | Â |
|---|---|
Number | 206 |
Sex, n (%) | Â |
Male Female Unknown | 119 (59.5%) 81 (40.5%) 6 |
Age (years), mean ± SD (range) |  |
Onset time Diagnosis time Duration | 22.7 ± 19.8 (0-77, n=146) 25.6 ± 18.0 (0.17-77, n=192) 3.5 ± 5.2 (0-31, n=139) |
Involvement, n (%) | Â |
Monostotic Polyostotic | 47 (22.8%) 159 (77.2%) |
Symptoms, n (%) | Â |
Pain Pathological fracture Swelling Dyspnea Chylothorax Nervous system impairment CSF leakage Hearing impairment | 141 (68.4%) 53 (25.7%) 43 (20.9%) 40 (19.4%) 39 (18.9%) 38 (18.4%) 14 (6.8%) 6 (2.9%) |
Treatment, n (%) | Â |
Surgery Bisphosphonates Sirolimus Interferon | 121 (66.9%) 103 (56.9%) 33 (18.2%) 32 (17.7%) |
Quality of life, n (%) | Â |
PR SD PD Dead Unknown | 92 (44.7%) 17 (8.3%) 11 (5.3%) 14 (6.8%) 72 (35.0%) |
Imaging evaluation, n (%) | Â |
PR SD PD Dead Unknown History of previous trauma, n (%) | 14 (6.8%) 74 (35.9%) 18 (8.7%) 14 (6.8%) 86 (41.7%) 35 (17.0%) |