Table 1 Clinical characteristics, airway morphology, and management outcomes of MKS cases (n = 5)
Cases | Age (years)/Sex | Diagnostic Delay (years) | Chief complaints | Transverse/sagittal diameter of the trachea (mm) | Right/left main bronchus diameter (mm)* | Treatment plan | Follow-up (months)/Outcome |
|---|---|---|---|---|---|---|---|
Case 1 | 86/Male | 20 | Chronic Cough, fever, Purulent Sputum | 42.1/43.5 | 18.0/14.0 | Antimicrobial and expectorant therapy | 1/death, multiorgan failure |
Case 2 | 65/Male | 0.25 | Chronic Cough, Purulent Sputum | 33.8/35.5 | 21.3/18.9 | Antimicrobial and expectorant therapy | 12/stable |
Case 3 | 46/Male | 2 | Chronic cough | 37.5/38.6 | 22.0/19.0 | Corticosteroids and bronchodilator aerosols | 60/stable |
Case 4 | 63/Female | 37 | Intermittent wheezing | 23.3/18.3 | 23.8/32.2 | Antimicrobial and expectorant therapy, intensive respiratory therapy, corticosteroids and bronchodilator aerosols | 60/stable |
Case 5 | 73/Male | 10 | Dyspnoea, Chronic Cough, Purulent Sputum | 29.5/31.5 | 22.3/24.6 | Antimicrobial and expectorant therapy, intensive respiratory therapy | 24/3 hospitalizations |