Table 3 Comparative classification systems for MKS
Types | Descriptions |
|---|---|
Anatomical Classification (Himalstein et al. [31]) | |
Type I | Relatively symmetrical, diffuse enlargement of the trachea and main bronchi |
Type II | The enlargement is more obvious and has a bizarre or eccentric configuration. There may be diverticula |
Type III | Diverticula or sacculations extend to the distal bronchi |
Aetiological Classification (Payandeh et al. [10]) | |
Type 1A | Infants who have undergone FETO as a therapy for antenatally diagnosed severe congenital diaphragmatic hernia and developed TBM |
Type 1B | Children or infants who developed TBM after prolonged intubation |
Type 2A | Patients who developed TBM after multiple pulmonary infections |
Type 2B | Patients who developed TBM after being diagnosed with pulmonary fibrosis |
Type 3 | Patients with TBM and evidence of extrapulmonary elastolysis |
Type 4 | Patients with TBM and no clear predisposing factors |